%0 Journal Article %T Demonstration of prion-like properties of mutant huntingtin fibrils in both in vitro and in vivo paradigms %+ Axe Neurosciences [CHU Québec] %+ Departement de Psychiatrie & Neurosciences, Université Laval, Québec, QC, Canada %+ Laboratoire des Maladies Neurodégénératives - UMR 9199 (LMN) %+ Department of Neurological Sciences, Rush University Medical Center, Chicago IL, USA %A Masnata, Maria %A Sciacca, Giacomo %A Maxan, Alexander %A Bousset, Luc %A Denis, Hélèna %A Lauruol, Florian %A David, Linda %A Saint-Pierre, Martine %A Kordower, Jeffrey %A Melki, Ronald %A Alpaugh, Melanie %A Cicchetti, Francesca %< avec comité de lecture %@ 0001-6322 %J Acta Neuropathologica %I Springer Verlag %V 137 %N 6 %P 981-1001 %8 2019-06 %D 2019 %R 10.1007/s00401-019-01973-6 %Z Life Sciences [q-bio]/Neurons and Cognition [q-bio.NC] %Z Life Sciences [q-bio]/Biochemistry, Molecular BiologyJournal articles %G English %L cea-02279743 %U https://cea.hal.science/cea-02279743 %~ CEA %~ CNRS %~ CEA-UPSAY %~ INSERM-SACLAY %~ UNIV-PARIS-SACLAY %~ CEA-UPSAY-SACLAY %~ JACOB %~ CEA-DRF %~ MIRCEN %~ TEST-HALCNRS %~ ANR %~ GS-ENGINEERING